A site for medical students - Practical,Theory,Osce Notes

>

What are Neurocutaneous diseases?

Cutaneous manifestations that are characteristic of certain neurological disease are described here
Tuberous sclerosis  is characterised by the following lesions
  • Adenoma sebaceum/Angiofibroma of face 
  • Subungual  fibroma
  • Shagreen patch
  • Leafy macule
Von Recklinghausen's disease
  • Multiple cutaneous and subcutaneous neurofibroma
  • Cafe-au-lait spots > 6 in no: >1.5 cm in size
  • Axillary freckles
Sturge Weber syndrome
Capillary hemangioma in trigeminal nerve distribution is seen in Encephalo-trigeminal angiomatosis
Hereditary hemorrhagic telangiectasia
There is multiple telangiectasia of skin, mucosa, and pulmonary system